Diagnosing Fabry disease typically involves a comprehensive evaluation of the patient's symptoms and complaints, followed by a series of diagnostic tests ordered by a physician.

Key diagnostic tests for Fabry disease include:

* Enzyme Activity Assay: This test measures the activity of the alpha-galactosidase A (alpha-GAL) enzyme in the blood. Levels at or below 1% of normal activity are indicative of Fabry disease.
* Genetic Testing: A genetic test, specifically DNA sequencing, may be requested by the physician to identify mutations in the GLA gene, which is responsible for Fabry disease.